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Immune System · Signaling Pathways · Autoimmune Diseases

Each column = one signaling pathway · Arrows ↓ = signal flow · Click any element for detailed explanation

⬡ Pathways ⚕ Diseases & Biologics 📚 Sources ◉ Ankylosing Spondylitis…
DISEASE

Ankylosing Spondylitis (Axial Spondyloarthritis)

Ankylosing spondylitis, now correctly termed axial spondyloarthritis (axSpA), is a chronic inflammatory disease primarily affecting the spine and sacroiliac joints. Typical features are chronic back pain that improves with movement and worsens at rest (inflammatory back pain), morning stiffness, and progressive spinal fusion through ossification (ankylosis). The disease usually begins in young adulthood and is strongly associated with the genetic marker HLA-B27 (about 85–95% of affected individuals carry this gene).

Immunologically, the IL-23/IL-17 axis is central: At the entheses (the sites where tendons and ligaments attach to bone), there are IL-23-responsive immune cells, including γδ T cells and ILC3 (innate lymphoid cells type 3), which produce IL-17 — interestingly often independently of classical Th17 cells. IL-17 promotes both inflammation and pathological new bone formation (syndesmophytes) leading to spinal fusion. TNF-α also plays an important role in sacroiliac joint inflammation and peripheral arthritis.

Biologics: Anti-TNF (infliximab, adalimumab, etanercept, golimumab, certolizumab) are the first approved biologic class and highly effective against pain and inflammation. Anti-IL-17A (secukinumab, ixekizumab) are also approved and particularly effective for axial inflammation. JAK inhibitors: Upadacitinib (JAK1) and tofacitinib (JAK1/3) are approved. However, anti-IL-23 antibodies (risankizumab) surprisingly showed no efficacy in axial SpA in studies — suggesting that IL-17 production at the entheses is partly IL-23-independent.

ALL TOPICS (click for details)
Pemphigus Vulgaris (Au… CIDP (Chronic Polyradi… Guillain-Barré Syndrom… Ulcerative Colitis (Ch… Type 1 Diabetes Mellit… Amyotrophic Lateral Sc… Polymyositis (Autoimmu… Sjögren's Syndrome (Au… Atopic Dermatitis (Ecz… Crohn's Disease (Infla… Systemic Lupus Erythem… Rheumatoid Arthritis (… Cutaneous Lupus Erythe… Multiple Sclerosis (MS… Psoriasis — Classical … Vasculitis (Blood Vess… Urticaria (Hives) B Cells and Plasma Cel… FLS — Synovial Fibrobl… Th2 Cells (T Helper 2 … Th17 Cells (The Inflam… Mast Cells (Allergy Ef… Dendritic Cells (Senti… Osteoclasts (Bone-Reso… Keratinocytes (Skin Ce… Macrophages (Phagocyte… Th1 Cells (T Helper 1 … Regulatory T Cells (Tr… Neutrophil Granulocyte… JAK1 — The Most Versat… TYK2 — The Most Elegan… JAK2 — Hematopoiesis a… JAK3 — The Immune Syst… The JAK/STAT Signaling… The IL-23/IL-17 Axis (… Type I Interferons & P… NF-κB — The Central In… TNF-α Signaling Pathwa… BAFF/APRIL — Survival …